| Adult presentation of Caroli's syndrome treated with orthotopic liver transplantation. | |
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MedLine Citation:
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PMID: 9382076 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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When Caroli's disease, defined as a congenital dilation and ectasia of segmental intrahepatic bile ducts in the absence of other histological abnormalities, is associated with periportal fibrosis, it is termed Caroli's syndrome. We describe the case of a 35-yr-old woman with Caroli's syndrome without clinical manifestation of portal hypertension despite diffuse involvement of the liver who was successfully treated with orthotopic liver transplantation after recurrent nearly fatal episodes of cholangitis. |
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Authors:
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T D Schiano; M I Fiel; C M Miller; H C Bodenheimer; A D Min |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: The American journal of gastroenterology Volume: 92 ISSN: 0002-9270 ISO Abbreviation: Am. J. Gastroenterol. Publication Date: 1997 Oct |
Date Detail:
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Created Date: 1997-11-12 Completed Date: 1997-11-12 Revised Date: 2004-11-17 |
Medline Journal Info:
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Nlm Unique ID: 0421030 Medline TA: Am J Gastroenterol Country: UNITED STATES |
Other Details:
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Languages: eng Pagination: 1938-40 Citation Subset: IM |
Affiliation:
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Department of Medicine, Mount Sinai Medical Center, New York, New York, USA. |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Adult Caroli Disease / pathology, surgery* Female Humans Liver / pathology Liver Transplantation* |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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