Document Detail


Adult-onset ataxia and polyneuropathy caused by mitochondrial 8993T-->C mutation.
MedLine Citation:
PMID:  16049925     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
The 8993T-->C mutation in mitochondrial DNA (mtDNA) has been described previously to be associated with infantile- or childhood-onset phenotypes, ranging from Leigh's syndrome to neurogenic weakness, ataxia, and retinitis pigmentosa syndrome. We report a kindred with adult-onset slowly progressive ataxia and polyneuropathy and with the heteroplasmic 8993T-->C mutation. Our findings suggest that the 8993T-->C mtDNA mutation should be considered in the differential diagnosis of nondominant adult-onset ataxia and axonal neuropathy.
Authors:
Maria T Rantamäki; Heidi K Soini; Saara M Finnilä; Kari Majamaa; Bjarne Udd
Related Documents :
19320655 - Early onset of renal cancer in a family with birt-hogg-dubé syndrome.
18089695 - Endocrine and radiological studies in patients with molecularly confirmed charge syndrome.
8466645 - Cytogenetic evidence of involvement of chromosome regions 15q12 and 12q15 in conditions...
20535495 - Analysis of the chn1 gene in patients with various types of congenital ocular motility ...
3594995 - Superficial posterior compartment syndrome of the leg with deep venous compromise. a ca...
1484695 - Encephalocraniocutaneous lipomatosis and oculocerebrocutaneous syndrome. a differential...
Publication Detail:
Type:  Comparative Study; Journal Article; Research Support, Non-U.S. Gov't    
Journal Detail:
Title:  Annals of neurology     Volume:  58     ISSN:  0364-5134     ISO Abbreviation:  Ann. Neurol.     Publication Date:  2005 Aug 
Date Detail:
Created Date:  2005-08-02     Completed Date:  2005-10-31     Revised Date:  2006-11-15    
Medline Journal Info:
Nlm Unique ID:  7707449     Medline TA:  Ann Neurol     Country:  United States    
Other Details:
Languages:  eng     Pagination:  337-40     Citation Subset:  IM    
Affiliation:
Department of Physical Medicine and Rehabilitation, Seinäjoki Central Hospital, Seinäjoki, Finland. maria.rantamaki@epshp.fi
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Adult
Aged
Ataxia / genetics*
DNA Mutational Analysis / methods
DNA, Mitochondrial / genetics*
Female
Humans
Male
Middle Aged
Mutation*
Pedigree
Point Mutation
Polyneuropathies / genetics*
Chemical
Reg. No./Substance:
0/DNA, Mitochondrial

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  Magnetic resonance imaging study in older fragile X premutation male carriers.
Next Document:  Meniscal regeneration using tissue engineering with a scaffold derived from a rat meniscus and mesen...