Document Detail

Adult Hirschsprung's disease presenting as sigmoid volvulus: a case report and review of literature.
MedLine Citation:
PMID:  16969608     Owner:  NLM     Status:  MEDLINE    
Sigmoid volvulus is a rare presentation of Hirschsprung's disease. A 38-year-old male presented with acute intestinal obstruction and a history of chronic constipation since childhood. Abdominal radiographs showed megarectum and megacolon with dissipated feces. Sigmoidoscopy revealed gangrenous bowel mucosa affecting the sigmoid colon. Emergency laparotomy revealed a grossly dilated bowel with concurrent gangrenous sigmoid volvulus. He was treated successfully with proctocolectomy with J-pouch-anal anastomosis and a defunctioning ileostomy. Histological analysis was consistent with short segment Hirschsprung's disease. Although uncommon, adult Hirschsprung's disease is a cause of chronic constipation and can present acutely with a sigmoid volvulus. Mortality in cases with sigmoid volvulus is greater than in cases without (15.4% vs. 0%). A better awareness of this condition will facilitate management.
F L S Tan; Y-M Tan; S M Heah; F Seow-Choen
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Publication Detail:
Type:  Case Reports; Journal Article     Date:  2006-09-20
Journal Detail:
Title:  Techniques in coloproctology     Volume:  10     ISSN:  1123-6337     ISO Abbreviation:  Tech Coloproctol     Publication Date:  2006 Oct 
Date Detail:
Created Date:  2006-10-09     Completed Date:  2007-01-19     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9613614     Medline TA:  Tech Coloproctol     Country:  Italy    
Other Details:
Languages:  eng     Pagination:  245-8     Citation Subset:  IM    
Department of General Surgery, Singapore General Hospital, Singapore.
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MeSH Terms
Hirschsprung Disease / complications*,  diagnosis*,  surgery
Intestinal Volvulus / etiology*,  radiography,  surgery
Sigmoid Diseases / etiology*,  radiography,  surgery

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