Document Detail


Adipsic hypernatremia and bilateral renal stones in a child with ectrodactyly-ectodermal dysplasia-cleft lip-palate (EEC) syndrome.
MedLine Citation:
PMID:  20681222     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
EEC syndrome an autosomal dominant disorder with variable expression and cardinal signs of ectrodactyly, ectodermal dysplasia, and orofacial clefts. In this report, we describe a patient with EEC syndrome, adipsic hypernatremia without brain anomalies, and bilateral renal stones, two manifestations that were not reported before.
Authors:
R M Shawky; S M Elsayed; D I Sadik; S Gad; N S Seifeldin
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Genetic counseling (Geneva, Switzerland)     Volume:  21     ISSN:  1015-8146     ISO Abbreviation:  Genet. Couns.     Publication Date:  2010  
Date Detail:
Created Date:  2010-08-04     Completed Date:  2010-09-03     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9015261     Medline TA:  Genet Couns     Country:  Switzerland    
Other Details:
Languages:  eng     Pagination:  215-20     Citation Subset:  IM    
Affiliation:
Pediatrics Department, Faculty of Medicine, Ain Shams University, Cairo, Egypt. shawkyrabah@yahoo.com
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MeSH Terms
Descriptor/Qualifier:
Abnormalities, Multiple*
Cleft Lip*
Cleft Palate*
Ectodermal Dysplasia*
Humans
Hypernatremia*
Infant
Kidney Calculi
Male
Syndrome

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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