| Acute airway obstruction in Hunter syndrome. | |
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MedLine Citation:
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PMID: 9780074 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Hunter syndrome is one of the mucopolysaccharidoses, characterized by a deficiency of the lysosomal enzyme iduronate sulfatase. Among its physical manifestations, there are numerous head and neck signs, including characteristic facial features, macroglossia and short neck. The accumulation of glycosaminoglycans in the soft tissues of the head and neck can be associated with acute airway obstruction. We report a 7 year old boy with Hunter syndrome who developed acute airway compromise requiring an emergency tracheotomy. A review of the literature of airway management in patients with this disease is also presented. |
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Authors:
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A Yoskovitch; T L Tewfik; R T Brouillette; M D Schloss; V M Der Kaloustian |
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Publication Detail:
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Type: Case Reports; Journal Article; Review |
Journal Detail:
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Title: International journal of pediatric otorhinolaryngology Volume: 44 ISSN: 0165-5876 ISO Abbreviation: Int. J. Pediatr. Otorhinolaryngol. Publication Date: 1998 Aug |
Date Detail:
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Created Date: 1998-12-22 Completed Date: 1998-12-22 Revised Date: 2005-11-16 |
Medline Journal Info:
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Nlm Unique ID: 8003603 Medline TA: Int J Pediatr Otorhinolaryngol Country: IRELAND |
Other Details:
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Languages: eng Pagination: 273-8 Citation Subset: IM |
Affiliation:
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Department of Otolaryngology, McGill University, Montreal, Quebec, Canada. |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Airway Obstruction
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etiology*,
surgery Child Humans Male Mucopolysaccharidosis II / complications* Tracheotomy |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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