Document Detail


Absent ulna in the Klippel-Feil syndrome: an unusual associated malformation.
MedLine Citation:
PMID:  7363502     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
A patient is reported with a severe type 2 Klippel-Feil syndrome, and absent ulna and ulnar ray. The severity of the musculo-skeletal involvement did not allow for corrective procedures. This uncommon association of skeletal malformations has not been previously reported. Since this syndrome has been described in families as a possible autosomal recessive trait, a 25% recurrence risk and the possibility of prenatal detection by fetal visualization methods should be taken into consideration.
Authors:
J Chemke; R Nisani; R E Fischel
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Clinical genetics     Volume:  17     ISSN:  0009-9163     ISO Abbreviation:  Clin. Genet.     Publication Date:  1980 Feb 
Date Detail:
Created Date:  1980-06-25     Completed Date:  1980-06-25     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  0253664     Medline TA:  Clin Genet     Country:  DENMARK    
Other Details:
Languages:  eng     Pagination:  167-70     Citation Subset:  IM    
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MeSH Terms
Descriptor/Qualifier:
Female
Humans
Infant
Klippel-Feil Syndrome / genetics*,  radiography
Ulna / abnormalities*,  radiography

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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