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Finsterer Josef J Krankenanstalt Rudolfstiftung , Vienna , - - 2014
Objectives: Stress-induced cardiomyopathy (takotsubo-syndrome, TTS) and its recurrence have not been described in myotonic dystrophy-1. Case report: The patient was a 47-year-old female who was suspected to suffer from myotonic dystrophy-1 at 20 years of age, upon the typical clinical presentation and the electrophysiological findings. During weaning from general anesthesia ...
Masood Muhammad Qamar MQ Department of Medicine, The Aga Khan University Hospital, Karachi, - - 2014
Objective: To describe two cases of Sheehan's syndrome who presented with ventricular tachycardia.Methods: In this case series we present two cases of Sheehan's syndrome who presented with ventricular tachycardia which is an extremely rare complication of Sheehan's syndrome. We reviewed the literature for cases of panhypopituitarism presented with ventricular tachycardia. ...
Antonini-Canterin Francesco F aCardiologia Preventiva e Riabilitativa, ARC, Azienda Ospedaliera S. Maria degli Angeli, Pordenone bCardiologia, Ospedale S. Antonio, San Daniele del Friuli cMedicina Interna, Ospedale Villa Sofia, Palermo dCardiologia, Università di Pisa, Pisa eCardiologia, Università di Messina, Messina, Italy f'Carol Davila' University of Medicine and Pharmacy, 'Prof. Dr C.C. Iliescu' Institute of Cardiovascular Diseases, Bucharest, Romania gCardiologia, ARC, Azienda Ospedaliera S. Maria degli Angeli, Pordenone, - - 2014
The aims of the study were to evaluate whether a further classification of metabolic syndrome according to the number of traits (based on the Adult Treatment Panel III definition) could better explain the impact on cardiovascular remodeling and function, and to assess the role of single metabolic syndrome components in ...
Sadick Victoria J VJ Faculty of Medicine, Dentistry and Health Science, University of Western Australia, Perth, - - 2014
A 52 year-old male with Klinefelter syndrome presented with chest tightness and rapid atrial fibrillation with hypotension. His echocardiogram demonstrated symmetrical left ventricular hypertrophy with minimal diastolic dysfunction. Subsequent investigations confirmed the diagnosis of Fabry cardiomyopathy. This is the first reported case of Klinefelter syndrome with homozygous sex-linked recessive mutation ...
Borregaard Rune R Department of Cardiology, Aarhus University Hospital Skejby, Brendstrupgaardsvej 100, DK-8200 Aarhus N, Denmark - - 2014
To assess the long-term mortality and occurrence of post-ablation atrial fibrillation in patients undergoing a radiofrequency ablation for the Wolff-Parkinson-White (WPW) syndrome. A retrospective cohort study of patients (N = 362) subjected to radiofrequency ablation of the WPW syndrome at Aarhus University Hospital from 1990 to 2011. A comparison cohort ...
Toyota Naoki N Department of Pediatric Cardiology, National Cerebral and Cardiovascular Center, Osaka, Japan, - - 2014
We present a case of a high-risk 19-year-old female with long-QT syndrome (LQTS) with compound mutations. She had a history of aborted cardiac arrest and syncope and had received treatment with propranolol for 15 years. However, because she developed adult-onset asthma we tried to switch propranolol, a nonselective beta-blocker, to beta-1-cardioselective ...
Knapper Joseph T JT Department of Medicine and Division of Cardiology), Emory University, Atlanta, - - 2014
Platypnea-orthodeoxia syndrome (POS) is a rare but clinically important form of dyspnea. The syndrome is characterized by dyspnea and arterial oxygen desaturation that occurs in the upright position and improves with recumbency. In cardiac POS, an atrial septal defect or patent foramen ovale allows communication between the right- and left-sided ...
McCrossan Brian B 1Department of Paediatric Cardiology,Murdoch Children's Research Institute and University of Melbourne,Royal Children's - - 2014
Long QT syndromes encompass the most prevalent group of ion channelopathies. Long QT syndromes are predominantly familial and predispose the affected individual to ventricular arrhythmias and sudden death. Permanent pacemaker insertion for long QT syndrome is discouraged apart from younger patients exhibiting 2:1 atrioventricular block. However, permanent pacemaker insertion is ...
Ahmad Farook F Department of Medicine, University Malaya Medical Centre, 50603, Kuala Lumpur, - - 2014
Pulmonary hypertension is frequently associated with atrial septal defect and various connective tissue disorders. This case describes a 74-year-old woman who presented with symptoms of heart failure and concomitant involvement of salivary glands and keratoconjunctivitis. An echocardiogram demonstrated ostium secundum atrial septal defect with left to right shunt and severe ...
Rudic Boris B 1st Department of Medicine, University Medical Centre Mannheim, Germany; DZHK (German Centre for Cardiovascular Research), partner site Mannheim, - - 2014
A 44-year-old female was admitted due to appropriate ICD shock delivery after ventricular fibrillation (VF). The patient was diagnosed with long-QT syndrome (LQTS) previously and had received a dual-chamber ICD for secondary prevention (Boston Scientific, Teligen 100 F110). This article is protected by copyright. All rights reserved.
Kram Yoseph Aaron YA Department of Otolaryngology-Head and Neck Surgery, University of California San Francisco, San Francisco, CA, - - 2014
Silent SINUS SYNDROME is a clinical syndrome defined by unilateral maxillary sinus opacification with atelectasis of the uncinate process. Clinically, this disorder is characterized by enophthalmos and hypoglobus. The current case report illustrates dramatic bony remodeling of the maxillary sinus following maxillary antrostomy. Although the remodeling is noted in the ...
Kilinc Ozden O Marmara University, Department of Neurology, Istanbul, Turkey. Electronic address: - - 2014
Congenital bilateral perisylvian syndrome (CBPS) is a type of cortical developmental abnormality associated with distinctive clinical and imaging features. Clinical spectrum of this syndrome is quite heterogeneous, with different degrees of neurological impairment in affected individuals. High-definition magnetic resonance imaging (MRI) has a great importance in revealing the presence of ...
Heyer Geoffrey L GL Division of Pediatric Neurology, Nationwide Children's Hospital and Department of Neurology at The Ohio State University, Columbus, OH. Electronic address: - - 2014
Little is known about the effectiveness of abdominal and lower-extremity compression in treating postural tachycardia syndrome, particularly in younger patients. This repeated-measures study of 20 young patients with postural tachycardia syndrome demonstrates that compression during head-upright tilt table testing decreases tachycardia (P < .001) and effectively attenuates orthostatic symptoms.
Rotstein Dalia L DL Division of Neurology, Department of Medicine, University of Toronto, Toronto, Ontario, - - 2014
Neurologists must entertain a broad differential diagnosis when considering a patient with cavernous sinus syndrome, including neoplasm, trauma, vascular causes, inflammatory processes, and infections. We report the case of a 37-year-old woman initially diagnosed with cavernous sinus syndrome, where subsequent investigations revealed findings of Takayasu's arteritis, a large vessel vasculitis. ...
Kukla Piotr P Department of Cardiology and Internal Medicine, Specialistic Hospital, Gorlice, Poland, 38-300 Gorlice, Wegierska Street 21, Poland. - - 2014
Andersen -Tawil syndrome (ATS) is an autosomal -dominant or sporadic disorder characterized by ventricular arrhythmias, periodic paralysis, and distinctive facial and skeletal dysmorphism. Mutations in KCNJ2, which encodes the α-subunit of the potassium channel Kir2.1, were identified in patients with ATS. This genotype has been designated as type-1 ATS (ATS1). ...
Bayés de Luna Antonio - - 2014
Brugada syndrome is a genetically determined familial disease with autosomal dominant transmission and variable penetrance, conferring a predisposition to sudden cardiac death due to ventricular arrhythmias. The syndrome is characterized by a typical electrocardiographic pattern in the right precordial leads. This article will focus on the new electrocardiographic features recently ...
Shinohara Tetsuji T Department of Cardiology and Clinical Examination, Faculty of Medicine, Oita University, Oita, Japan. Electronic address: - - 2014
Brugada syndrome and idiopathic ventricular fibrillation (VF) associated with infero-lateral early repolarization patterns are termed "J-wave syndromes". In such patients, an implantable cardioverter-defibrillator (ICD) is first-line therapy for prevention of sudden cardiac death. However, frequent ICD shocks due to recurrent VF remain serious problems. We wished to ascertain if combination ...
Dohadwala Mustafa M Department of Medicine, The Cardiac Arrhythmia Center, Tufts Medical Center, 800 Washington Street, Box #197, Boston, MA 02111, - - 2014
Sudden death is often the first manifestation in inherited cardiac arrhythmia syndromes. Patients with long QT syndrome who have an episode of syncope while on beta-blockade should be offered an implantable cardioverter-defibrillator (ICD). In Brugada syndrome and hypertrophic cardiomyopathy, ICDs are often the most effective treatment of primary and secondary ...
Zhao Juan J Department of Pediatrics, Peking University First Hospital, Beijing 100034, - - 2014
The abnormal blood volume regulation is one of the most important pathogenesis in postural tachycardia syndrome in children. This study was designed to investigate the plasma atrial natriuretic peptide and antidiuretic hormone levels in postural tachycardia syndrome children, and their associations with the changes in heart rate and blood pressure ...
Shu Juan J Department of Cardiology, the First Hospital, Xi'an Jiaotong University, Xi'an, - - 2014
A 5-year-old female child with bilateral hand syndactyly, QT prolongation and 2:1 atrioventricular (AV) block was seen in consultation. The genetic testing identified a mutation in CACNA1C gene, confirming type 1 Timothy syndrome (LQT8). This article is protected by copyright. All rights reserved.
Cecilia Gonzalez M GM Department of Pediatric Cardiology and Pediatric Intensive Care, Cliniques Universitaires St Luc, Brussels, - - 2014
Torsades de Pointes is an extremely rare arrhythmia in children associated to LQT syndrome. Pheochromocytomas are also extremely rare tumours in the paediatric age. We present a case of a young patient with an acquired long QT syndrome complicating with Torsades de Pointes as first clinical manifestation of a pheochromocytoma.
Mazzanti Andrea A Molecular Cardiology, IRCCS Salvatore Maugeri Foundation, Pavia, - - 2014
Up to 14,500 young individuals die suddenly every year in Europe of cardiac pathologies. The majority of these tragic events are related to a group of genetic defects that predispose the development of malignant arrhythmias (inherited arrhythmogenic diseases [IADs]). IADs include both cardiomyopathies (hypertrophic cardiomyopathy, arrhythmogenic right ventricular cardiomyopathy, dilated ...
Olde Nordkamp L R A LR Heart Center, Department of Cardiology, Academic Medical Centre, PO Box 22700, 1100 DE, Amsterdam, the - - 2014
Treating therapy-resistant patients with inherited arrhythmia syndromes can be difficult and left cardiac sympathetic denervation (LCSD) might be a viable alternative treatment option. We provide an overview of the indications and outcomes of LCSD in patients with inherited arrhythmia syndromes in the only tertiary referral centre in the Netherlands where ...
Hocini Mélèze M Institut LIRYC, Hôpital Cardiologique du Haut Lévêque, Université Victor Segalen Bordeaux II, Bordeaux, Pessac, - - 2014
Inherited arrhythmia disorders associated with structurally normal heart (i.e. long and short QT syndrome, Brugada syndrome, catecholaminergic polymorphic ventricular tachycardia, early repolarization syndrome, idiopathic ventricular fibrillation) cause 10% of 1.1 million sudden deaths in Europe and the USA. The purpose of this European Heart Rhythm Association (EHRA) electrophysiology wire survey ...
Fugate Jennifer E JE Division of Critical Care Neurology, Department of Neurology. Electronic address: - - 2014
To describe causes, manifestations, and diagnosis of serotonin syndrome following therapeutic hypothermia (TH) after cardiac arrest METHODS: Retrospective case series from a tertiary academic medical center RESULTS: Three male patients suffered witnessed out-of-hospital cardiac arrests and were treated with induced TH. Initial cardiac rhythms included asystole in two and ventricular ...
Natasha Barrios - - 2014
Dermoid sinus is an uncommon epithelial-lined fistula that may be associated with vertebral malformations. In humans, Klippel-Feil syndrome (KFS) is a rare condition characterized by congenital cervical vertebral fusion and may be associated with other developmental defects, including dermoid sinus. The present case report describes an adult Dachshund with cervical ...
Değirmencioğu Aleks A Department of Cardiology, Acıbadem University Faculty of Medicine, İstanbul, Turkey. - - 2014
We report a 68-year-old man who presented with heart failure and atrial fibrillation (AF) with rapid ventricular response and wide QRS complexes. Tachycardia-induced cardiomyopathy (TIC) due to persistent AF developing on the basis of Wolff-Parkinson-White (WPW) syndrome was considered. Signs and symptoms of heart failure improved with restoration of sinus ...
Kurtulmuş Seçil S Department of Maternity and Gynecology, Ege Training and Research Hospital, İzmir, - - 2014
We aimed to present a fetus with Meckel-Gruber syndrome (MKS) who had left atrial isomerism, heterotaxy syndrome and complete heart block. A 26-year-old healthy female was referred to our clinic in the 23rd week of her pregnancy. The fetus had multiple systemic anomalies including fetal heart. Fetal echocardiography revealed a ...
Van Asbroeck P J - - 2014
Acquired long-QT syndrome is an iatrogenic disorder, usually induced by drugs, which can cause life-threatening arrhythmias. We present a case report on an acquired long-QT syndrome with an interesting confluence of circumstances, and comment on aetiology and treatment.
Steiner Robert - - 2014
First presented by Brugada and Brugada in 1992, Brugada Syndrome (BrS) is a primary electrical disease of the heart that causes sudden cardiac death or life-threatening ventricular arrhythmias. This disease is hereditary autosomic dominant transmitted and genetically determined. The syndrome has been linked to mutations in SCN5A, the gene encoding ...
Kaiser Elisabeth E Heart Institute (Incor), Hospital das Clínicas da Faculdade de Medicina da Universidade de São Paulo, - - 2014
The association between Brugada syndrome (BS) and ventricular preexcitation is a rare condition, with sporadic cases already reported. We report the case of a 29-year-old man, with palpitation unrelated to physical or emotional stress. The electrocardiogram of the first visit revealed a ventricular preexcitation pattern and an end-conduction delay, with ...
Escobar-Diaz Maria C MC Department of Cardiology, Boston Children's Hospital, 300 Longwood Avenue, Boston, MA, 02115, USA, - - 2014
Congenital atrioventricular (AV) block is commonly associated with heterotaxy syndrome; together they have reportedly low survival rates (10-25 %). However, information about perinatal outcome and predictors of non-survival after prenatal diagnosis of this association is scarce. Therefore, we studied fetuses with heterotaxy syndrome and bradycardia or AV-block diagnosed between 1995 and ...
Tempelhof Michael M Northwestern University, 251 East Huron Street, Feinberg 08-503, Chicago, IL 60611 USA. - - 2014
Superior vena cava (SVC) syndrome is a complication resulting from long-term residence of leads or in-dwelling catheters at the SVC to right atrial (RA) junction. SVC syndrome management is complicated by variable responses to anticoagulation therapies and technically challenging interventional procedures, such as balloon dilatation or stent placement at the ...
Kowalczyk Ewelina - - 2014
We describe a patient with severe hypothermia, in whom the electrocardiogram showed giant J-waves, also known as Osborn waves, distinguishable in the inferior and anterolateral leads. Moreover, a Brugada-like pattern was also visible in leads V2 and V3. The presented case and ECG findings may contribute to the discussion about ...
Takaya Yoichi Y Department of Cardiovascular Medicine, Okayama University Graduate School of Medicine, Dentistry and Pharmaceutical Sciences, Okayama, - - 2014
Platypnea-orthodeoxia is a rare condition characterized by dyspnea and oxygen desaturation induced by the upright position and relieved by recumbency. The most common cause of this syndrome is right-to-left shunt through interatrial communications such as patent foramen ovale (PFO) or atrial septal defect (ASD). In addition, this syndrome can be ...
Nelson Jessie G JG Emergency Medicine Department, Regions Hospital, St. Paul, Minnesota; Department of Emergency Medicine, University of Minnesota, Minneapolis, - - 2014
Atrial flutter with 1:1 atrioventricular conduction via an accessory pathway is an uncommon presentation of Wolff-Parkinson-White syndrome not previously reported in the emergency medicine literature. Wolff-Parkinson-White syndrome, a form of ventricular preexcitation sometimes initially seen and diagnosed in the emergency department (ED), can present with varied tachydysrhythmias for which certain ...
McKinnie J E JE Department of Anesthesiology, University of Tennessee Health Sciences Center, Memphis, TN, - - 2014
Oral-Facial-Digital syndrome or Mohr syndrome is a rare congenital disorder characterized by malformations of face, oral cavity, laryngeal structures, trachea, and digits, muscular-skeletal abnormalities, and congenital cardiac defects. In this case report, we describe the anesthetic management of a parturient with Oral-Facial-Digital syndrome type II and repaired tetralogy of Fallot ...
Goto Hiroko H Gifu Prefectural General Medical Center, Gifu, - - 2014
T-wave alternans (TWA), a beat-to-beat fluctuation in T wave morphology and QT interval, is commonly observed in patients with congenital long-QT syndrome (LQTS). However, only a few studies have focused on changes within the QRS complex during TWA. We report a case of LQTS who exhibited prominent QRST-wave alternans (QRSTWA) ...
Maher Patrick Joseph - - 2014
ABSTRACTFeatures consistent with the syndrome known as excited delirium (ExDS) have been associated with law enforcement restraint-related death. The pathophysiology and exact causative factors of restraint-related death associated with ExDS remain unclear. We present a case of successful field resuscitation of a man with ExDS who experienced cardiopulmonary arrest while ...
Vadivelu Ramalingam R Department of Cardiology, Advanced Cardiac Centre, Post Graduate Institute of Medical Education and Research, Chandigarh, - - 2014
An 18-year-old male with Lutembacher's syndrome underwent balloon mitral valvotomy (BMV) and device closure of the atrial septal defect (ASD). BMV necessitated technical modification of taking the Inoue balloon over the wire (OTW) into the left ventricle (LV). The procedure was complicated by slippage of ASD device into the right ...
Otteno Helen H 0000-0001-9523-9038 Department of Obstetrics and Gynecology, Quillen College of Medicine, East Tennessee State University, Johnson City, TN 37604, - - 2014
An 82-year-old female presented with longstanding history of both painful bladder syndrome and atrial fibrillation. She underwent hydrodistension remarkable for hematuria without temporary discontinuation of Dabigatran. Subsequently, patient was admitted to the hospital secondary to anemia and hemorrhagic cystitis.
Gysel Michael M 0000-0002-9897-5038 Department of Medicine, Kingston General Hospital, Queen's University, Kingston, ON, Canada K7L - - 2014
A 71-year-old woman collapsed while working as a grocery store cashier. CPR was performed and an AED revealed torsades de pointes (TdP). She was subsequently defibrillated resulting in restoration of sinus rhythm with a QTc interval of 544 msec. Further evaluation revealed a diagnosis of Takotsubo Cardiomyopathy (TCM) contributing to the ...
Gan Weh Loong WL Department of Ophthalmology, Pennine Acute Hospitals NHS Trust, Royal Oldham Hospital, Oldham, - - 2014
An uncommon case of unilateral painless enophthalmos in a 44-year-old woman is presented. Despite the noticeable orbital asymmetry caused by enophthalmos, the patient has normal visual acuities in both eyes with unremarkable ophthalmic examination. Diagnosis of silent sinus syndrome was confirmed on the CT orbits and paranasal sinuses, showing complete ...
Tester David J DJ Mayo Clinic, Rochester, - - 2014
Long QT syndrome (LQTS) is a potentially life-threatening cardiac arrhythmia characterized by delayed myocardial repolarization that produces QT prolongation and increased risk for torsades des pointes (TdP)-triggered syncope, seizures, and sudden cardiac death (SCD) in an otherwise healthy young individual with a structurally normal heart. Currently, there are three major ...
Brugada Ramon R University of Girona-IDIBGI, Girona, - - 2014
Brugada syndrome is a rare cardiac arrhythmia characterized by electrocardiographic right bundle branch block and persistent ST-segment elevation in the right precordial leads. It is associated with ventricular fibrillation and a high risk for sudden cardiac death, predominantly in younger males with structurally normal hearts. Patients can remain asymptomatic, and ...
Chryssostomidis Gregory G Department of Paediatric and Congenital Cardiac Surgery, Onassis Cardiac Surgery Centre, Athens, - - 2014
The Holt-Oram syndrome is a rare congenital disorder involving the skeletal and cardiovascular systems. It is characterized by upper limb deformities and cardiac malformations, atrial septal defects in particular. Four consecutive patients 1-15 years old with the Holt-Oram syndrome presented over a 10 year span for surgical treatment of their ...
Lambert Elisabeth E Human Neurotransmitters Laboratory, Baker IDI Heart and Diabetes Institute Melbourne, VIC, Australia ; Departments of Physiology, Monash University Clayton, VIC, - - 2014
Orthostatic intolerance is the inability to tolerate the upright posture and is relieved by recumbence. It most commonly affects young women and has a major impact on quality of life and psychosocial well-being. Several forms of orthostatic intolerance have been described. The most common one is the recurrent vasovagal syncope ...
Chockalingam Priya P Department of Clinical and Experimental Cardiology, Academic Medical Center, Meibergdreef 9, 1105AZ Amsterdam, The Netherlands. Electronic address: - - 2014
Inherited primary arrhythmias, namely congenital long QT syndrome, Brugada syndrome and catecholaminergic polymorphic ventricular tachycardia, account for a significant proportion of sudden cardiac deaths in young and apparently healthy individuals. Genetic testing plays an integral role in the diagnosis, risk-stratification and treatment of probands and family members. It is increasingly ...
- - 2013
Eisenmenger's syndrome is a condition due to any congenital heart defect with an intracardiac left-to-right communication that leads to pulmonary hypertension with reversed right-to-left blood flow and secondary cyanosis. The main complications of Eisenmenger's syndrome are heart failure and arrhythmias. Amiodarone, the drug of choice for arrhythmia treatment in such ...
Tepe Savaş S Department of Radiology, Bayındır Hospital, İstanbul, Turkey. - - 2013
We report herein an 83-year-old gentleman with lung cancer who presented with nausea, complete atrioventricular (AV) block and presyncope. Despite a present temporary pacemaker, which had been inserted through the femoral vein 5 days previously, the patient had asystole attacks that resolved with atropine administration. Coronary angiography demonstrated no critical ...
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