The Budd-Chiari syndrome is an uncommon condition in which hepatic venous outflow is obstructed by thrombosis of the major hepatic veins. Many of the cases are idiopathic, but it has been described in association with vena caval webs, abdominal trauma, retroperitoneal neoplasms, and hypercoagulable states. A patient with systemic lupus ...

A 49-year-old man with a past history of multiple episodes of acute pericarditis was admitted with a recurrence of symptoms combined with the superior vena caval syndrome. A bronchogenic cyst, located beneath the carina, was discovered. At operation, the cyst was partially resected, and superior vena caval flow was restored ...

A patient with acute leukaemia presenting with superior vena cava syndrome due to a large mediastinal mass is reported. The presence of blast cells with Auer rods in peripheral blood and bone marrow allowed the diagnosis of acute myeloblastic leukaemia. Following intensive chemotherapy the patient achieved a complete remission, with ...

A patient with an infarct limited to the paramedian thalamus and upper mesencephalon on the right side suffered a conjugate upgaze palsy associated with a monocular paresis of downward gaze in the ipsilateral eye (vertical "one-and-a-half" syndrome). This paresis involved tonic and phasic components. Vertical oculocephalic movements and conjugate horizontal ...

A case of Budd-Chiari syndrome associated with obstruction of the inferior vena cava is reported. The case was complicated by Sjögren's syndrome and chronic thyroiditis. A marked prolongation of activated partial thromboplastin time, due to circulating anticoagulant, was noted. Interrelation of thrombosis of the inferior vena cava, circulating anticoagulant, and ...

Congenital anomalies of systemic venous return have been associated with pacemaker complications. Awareness of the existence of these anomalies prior to catheterization can lead to the utilization of an alternate route for pacing, avoiding undue delay in the institution of pacing which may be urgently needed. Pulse Doppler echocardiographic demonstration ...

Thirteen patients who wore soft contact lenses were seen with a syndrome consistent with superior limbic keratoconjunctivitis. An irregular epithelial surface, punctate staining with fluorescein, and subepithelial infiltrates were found on the superior aspect of the corneas in association with hyperemia of the superior bulbar conjunctivae. The keratoconjunctivitis persisted as ...

Fifty-nine patients with a superior oblique palsy had a superior oblique tuck as part of their surgical treatment. The average size of the tuck was 12.0 mm. All cases had a decrease in the hyperdeviation in the primary position and some decrease in elevation in adduction in the operated eye ...

A patient who had had a functioning peritoneovenous (LeVeen) shunt for 10 months presented with recurrent ascites and the superior vena cava syndrome. He was found to have a thrombus occluding the superior vena cava and extending into the right atrium. The thrombus was removed and the shunt was declotted ...

A 56 year old man was seen because of recurrent right shoulder hemarthroses and a superior vena caval syndrome. Intermittent symptoms had occurred for six years and resulted in marked destructive changes in the right shoulder. Arthroscopy added pathological evidence of this unusual mechanism of arthropathy. Patients on anticoagulants deserve ...

Superior mesenteric artery syndrome (SMAS) was diagnosed in a 16-year-old boy who presented with a short history of repeated vomiting associated with weight loss to the point of collapse. After resuscitation and investigation, he was treated surgically and subsequently recovered well. The diagnostic difficulties and possible pathogenesis of SMAS are ...

The current status of surgery of the inferior vena cava, and the iliac and femoral veins in cases of phlebothrombosis, of postthrombotic syndrome, and in traumatic lesions is discussed. Each intervention in the venous system requires an exact preoperative diagnosis including phlebography and phlebodynamometry. After a mean observation period of ...

Recurrent superior mesenteric artery syndrome is an infrequent complication following reconstructive spinal surgery. However, if diagnosis and treatment are delayed, life-threatening dehydration and electrolyte abnormalities may occur. Recent advances in oral and parenteral alimentation have simplified the treatment of superior mesenteric artery syndrome following the early recognition of the characteristic ...

A patient is described in whom the nail changes of the yellow nail syndrome developed whilst she was taking penicillamine. Stopping the drug was associated with resolution of the nail changes. The yellow nail syndrome was first described in 1964 (Samman and White), but the cause is still unknown. Impaired ...

To our knowledge, this is the first reported clinicopathologic study of a patient with acquired inflammatory Brown's syndrome. The superior oblique tendon, trochlea, and anterior superior oblique muscle were surgically removed en bloc and studied by light microscopy. Surprisingly, the entire specimen was normal, without signs of inflammation or intrasheath ...

A young white woman who had been taking oral contraceptives for 8 yr presented with the Budd--Chiari syndrome. Stenosis of the hepatic segment of her inferior vena cava was observed and surgical correction was attempted, but she died of intravascular coagulation during the procedure. Postmortem examination showed myxoid intimal proliferation ...

The face of a child with Down's syndrome is stigmatised by the large tongue, open mouth, saddle nose and epicanthal folds. Operative reduction of macroglossia facilitates nose-breathing, comprehensible speech and eating. Raising the nasal bridge with Cialit-preserved homograft cartilage obliterates the epicanthal folds and conceals the oblique slant of the ...

The syndrome caused by the acute obstruction of the superior vena cava with central nervous system symptoms as well as with symptoms related to the oedema of the upper respiratory tract is often very severe and fatal to the patient. Conservative treatment is usually of no help, and consequently the ...

During the past 15 years a number of new symptoms, rarely seen in the past, have been observed with increasing frequency among Chinese schizophrenic patients. The authors identify the following symptoms: discordant (dissociative) syndrome, denial of lineage, delusion of leadership lineage, delusion of being married, child-bearing delusion, delusion of being ...

Local radioactive areas in the liver were observed as a result of superficial cavoportal shunting of radiocolloids in two patients with the inferior vena cava syndrome. In one patient a paraumbilical and/or a recanalized umbilical vein was apparently involved in the hepatopetal shunting. In the other patient a superficial anastomosis ...

Isotopic phlebography with Tc-99m-labeled microspheres was performed in 55 patients, 22 of whom presented with superior vena cava syndrome. The localization of the venous obstruction was visualized in each case, along with associated collateral views. Moreover, the transit times at different levels were markedly increased. In 11 patients, isotopic phlebography ...

Intrathoracic goiter is a rare cause of superior vena cava syndrome. We present the findings in a patient in whom the syndrome was precipitated by therapy with propylthiouracil and remitted on withdrawal of the medication. The superior vena cava syndrome did not recur on medical management, suggesting that surgery is ...

The superior vena caval syndrome is the clinical condition which develops at too high a pressure in the superior vena cava and the afferent veins. Its aetiology has changed in the course of time, but at present 97% of the cases are due to intrathoracic malignancy. An extremely rare aetiological ...

Congenital absence of the superior oblique tendon occurred in 18% of patients with a diagnosis of congenital superior oblique palsy who were treated with an attempt at a tuck of the superior oblique tendon. The presence of horizontal strabismus and amblyopia in a patient with diagnosis of congenital superior oblique ...

A case of superior vena cava syndrome secondary to longstanding benign obstructing disease is presented. A new method of surgical technique is detailed. Clinical manifestations, etiology, anatomy, diagnosis, and treatment of superior vena cava syndrome are reviewed and principles of successful surgical treatment of the venous system are elucidated. The ...

A case of afferent loop syndrome demonstrated by computed tomography (CT) is described. To our knowledge, no CT findings of this syndrome have been illustrated in the literature. This syndrome can be definitely diagnosed by CT when a U-shaped cystic mass continuous with the biliary system is demonstrated behind the ...

Four attempts to construct an arteriovenous fistula in the arms of a patient with chronic uremia resulted in occlusion of the fistulae. This was caused by superior vena cava syndrome which, in turn, was a late complication of transvenous pacing. A fistula was subsequently successfully constructed in a lower extremity.

Acute superior laryngeal palsy is often clinically unrecognized and frequently overlooked. Yet, this motor paralysis occurs more frequently than facial paralysis. Like acute facial paralysis, superior laryngeal palsy often occurs as part of a cranial polyneuritis that is probably related to herpes simplex virus reactivation. Rotation of the larynx and ...

Three cases of membranous obstruction of the inferior vena cava (IVC) are presented. Two of them underwent transcardiac membranotomy with good results. The third patient was treated symptomatically and died from gastrointestinal hemorrhage and hepatic coma two years after the diagnosis of Budd-Chiari syndrome. At autopsy, membranes were found in ...

Superior vena cava syndrome, a cause of severe distress, requires careful assessment of its etiology before therapy can be instituted. The diagnostic work-up is varied depending on whether or not the superior vena cava syndrome is associated with a mediastinal mass. Fine needle aspiration biopsy has proved to be of ...

A 50-year-old man presented with abdominal pain followed by marked liver and renal dysfunction. Although liver scan appearances were not diagnostic, at laparotomy a tense, enlarged liver was found with thrombosis of the inferior vena cava. Despite full supportive measures the patient died within a month of laparotomy. Subsequent necropsy ...

A 70-year-old man had the superior vena cava syndrome. At thoracotomy a retained central venous pressure line was found to be the cause of venous thrombosis at the outlet of the superior vena cava into the right atrium. A retained central venous pressure catheter and catheter-induced venous thrombosis should be ...

A 69-year-old man presented with acute stridor and was found to have the superior vena cava syndrome and bilateral laryngeal paresis. A clinical diagnosis of malignancy was made, but before any definite investigations could be made an emergency operation had to be performed to relieve the trachea. On operation the ...

A 37-year-old man with blastic crisis of chronic myelogenous leukemia was admitted for chemotherapy. After treatment with an infusion of vincristine, he became leukopenic and febrile. Two episodes of gram-negative septicemia were treated with prolonged courses of antibiotics; however, fever persisted, and the patient developed the superior vena cava syndrome. ...

The case history of a patient with Budd-Chiari syndrome (BCS) is described. The underlaying disease proved to be essential thrombocytosis. Congential elliptocytosis was also present. The value of the conventional liver scan, percutaneous splenoportoscintigraphy and isotopic phlebography of the inferior vena cava in the diagnosis of BCS is described. It ...

The so-called superior-mesenteric-artery syndrome is not mentioned in psychiatric journals or books. Yet two variations of the condition have been described. In its acute form, it can be mistaken for psychogenic vomiting in anorexic patients, while its chronic intermittent form is readily misdiagnosed as anorexia nervosa. The case report is ...

Budd-Chiari syndrome associated with protein-losing enteropathy is reported. A 26-year-old male suffered from ascites, edema in the lower extremities, and engorgement of ascending veins on the abdominal wall. The diagnosis of Budd-Chiari syndrome was made by inferior vena cavography. The 131I-polyvinylpyrrolidone test showed the association of protein-losing enteropathy. The surgical ...

The two cases of the superior vena caval syndrome described illustrate the problem of making a diagnosis and of determining the etiology of this syndrome. The cutaneous manifestations were typical of the syndrome and included the sudden onset of facial and upper extremity edema, erythema, and telangiectasia. The causes of ...

A patient is presented with the Budd-Chiari Syndrome. Because of a thrombosed inferior vena cava, none of the standard portal-systemic shunts could be utilized for decompression of the engorged liver. A new shunt constructed by interposing a Dacron graft between the superior mesenteric vein and the right atrium was performed. ...

A patient developed the superior vena cava syndrome from Nocardia asteroides pneumonia with mediastinitis. Specific treatment was dangerously delayed because malignancy was primarily suspected, and nocardial infection was not initially considered. The correct diagnosis was eventually made by appropriate stains and culture of a lung aspirate. Specific therapy with sulfonamide ...

The Counsellor modification of McIndoe's procedure was used to create a vagina in 12 of 15 patients who presented with Rokitansky-Kuster-Hauser syndrome. Eighty percent of these patients, followed postoperatively from 4 months to 8 years, report satisfactory coital function. Our experience suggests that a malleable stent fashioned to conform to ...

The superior vena cava syndrome is among the most important radiotherapeutic emergencies currently known. It is almost always due to malignant disease and therefore no time should be wasted in establishing the histological diagnosis of the malignant tumor which causes the superior vena cava obstruction. The conventional slow, low-dose irradiation ...

Superior vena cava syndrome developed in 4 of 1,000 patients in whom a transvenous pacemaker had been implanted. In all cases, endocardial leads were inserted through the cephalic vein and positioned at the apex of the right ventricle. The classical signs and symptoms of superior vena cava hypertension were observed ...

Duodenal compression by the superior mesenteric artery is the postulated cause of the superior mesenteric artery syndrome. Our case, as well as 2 other cases of renal vein compression reported in the literature, suggests that this is uncommon but should occur more frequently in this syndrome because it is anatomically ...

Benign lesions of the mediastinum rarely produce obstruction of the innominate vessels. Two patients with intrathoracic goitre are described who presented with the superior vena cava syndrome. Venography in each case demonstrated the extent of obstruction and degree of collateral circulation. Early recognition of the association of intrathoracic goitre and ...

The effects of diathermy to the trigone and upper urethra in the female urethral syndrome are compared with the effect of cystoscopy alone in the 27 cases. It is shown that the addition of diathermy gives superior results. The effects of such diathermy in the female urethral syndrome in 56 ...

Superior orbital fissure syndrome is a symptomatologic complex, consisting of retroorbital pain, paralysis of extraocular muscles, impairment of first trigeminal branches and frequent involvement of the optic nerve. From a review of 130 published cases including two personal observations, it appears that the clinical subdivisions and the several eponymic differentiations ...

A recent case of Lipiodol Ultrafluid embolism to the brain is reported. Pathogenetic concepts involving right-to-left shunts, and lympho-venous shunts with pulmonary capillary overloading are reviewed. In addition, it is suggested that a local disturbance in cerebral circulation due to a cava superior syndrome may contribute to the severe cerebral ...

The present report deals with a double-blind study comparing the new butyrophenone derivative, bromperidol, with haloperidol as the reference substance. Both substances were found to be highly effective in the treatment of psychotic syndromes belonging predominantly to the schizophrenia group. Certain clues, including the onset of action, seem to be ...

Of the three cases of superior mesenteric artery (Wilkie's) syndrome presented, one was associated with anorexia nervosa; this association has not been reported before. Two patients were treated surgically with a duodenojejunostomy, and one was treated medically. Vascular compression of the duodenum is a controversial subject. The syndrome probably is ...