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Results 351 - 400 of 563
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Anjum M I - - 1996
Interstitial cystitis is an uncommon disease reported predominantly in females. Recently we were involved in the management of 4 men who had the clinical, endoscopic and pathological features consistent with the diagnosis of interstitial cystitis. The rarity of occurrence of the disease in males prompted us to report these cases.
Ordoukhanian E - - 1995
In most western countries, scurvy has become a rare clinical entity. However, it may still be encountered in selected situations. It can mimic connective tissue disease, because of multiorgan involvement. Panniculitis has not previously been described in association with scurvy.
Ladocsi L T - - 1995
We report 3 cases of eosinophilic granulomatous cystitis in children. All presented with hematuria, urinary urgency, and dysuria. Treatment with oral corticosteroids led to rapid and complete recovery in 2 of the 3 cases. In the third case recovery was prolonged without the use of steroids. Because of the presumed ...
Treem WR - - 1995
Advances in the ability to treat primary causes of chronic liver disease in the adolescent have highlighted the importance of making a prompt diagnosis. Using a case study, this article reviews the clinical findings suggestive of chronic liver disease and the causes responsible in the adolescent. As the case evolves, ...
Green H D - - 1995
Gorham's disease (disappearing bone disease, massive osteolysis, idiopathic osteolysis, essential osteolysis, progressive atrophy of bone, spontaneous absorption of bone, phantom bone, hemangiomatosis/lymphangiomatosis of bone, progressive osteolysis) is an extremely rare occurrence. There are fewer than 150 reported cases in the literature. This disorder can be characterized by spontaneous or posttraumatic ...
Müller C - - 1995
Idiopathic adulthood ductopenia is a chronic cholestasic liver disease of unknown etiology characterized by the loss of interlobular bile ducts. We describe three patients who fulfilled the diagnostic criteria of idiopathic adulthood ductopenia, but differed from the cases reported so far in late manifestation of the disease and a benign ...
Elder D E - - 1995
OBJECTIVE: To highlight the clinical features of neonatal herpes simplex (HSV) infection that might facilitate earlier diagnosis. METHODOLOGY: Fifteen year retrospective review of proven neonatal HSV cases from a regional neonatal referral unit. RESULTS: Fifteen cases reviewed: 10 with central nervous system (CNS) disease, three with skin, eyes or mouth ...
Brantley D - - 1995
Elephantiasis is an uncommon disease in the United States. We present a case of nonfilarial elephantiasis nostras verrucosa in a 14-year-old girl. Most commonly, the upper and lower extremities are affected; the disease, in this patient, was confined to the buttock. The patient has done well after excision and primary ...
Kim M - - 1995
Rosai-Dorfman disease is a rare idiopathic histioproliferative disease affecting the lymph nodes. Extranodal involvement has also been recognized, but central nervous system manifestations are extremely rare. Only 12 patients with intracranial involvement have been reported previously, and they all presented with clinical and radiological findings suggestive of meningioma. We report ...
Mohan H - - 1995
A 21-year-old male from Kerala, south India, who had been living in Chandigarh for the last 4 years presented with a nasal polyp in the left nasal cavity. On histopathological examination, it was found to be due to rhinosporidiosis. This disease is not uncommon in south India, but few case ...
DiSaia P J - - 1995
Two cases of recurrent noninvasive Paget's disease of the vulva in a split-thickness graft without an underlying adenocarcinoma are presented. This is the third report of recurrence of extramammary Paget's disease in a split-thickness graft, and the second of such an occurrence without an underlying dermal adnexa adenocarcinoma. A hypothesis ...
Tan T Q - - 1995
Whipple's disease is a rare, chronic, multisystem illness that is pathologically characterized by the accumulation of macrophages in the involved tissue that have a positive periodic acid-Schiff reaction. It is typically seen in middle-aged white men, and only four cases involving persons younger than 15 years of age have been ...
Carter N - - 1995
We report two cases of elderly women who died unexpectedly. In both cases, light- and electron-microscopical examination proved a diagnosis of Fabry's disease. The major pathological changes were myocardial mottling, foamy vacuolation of myocytes and glomerular endothelial cells, and characteristic lamellar inclusions. Neither woman had either a personal or family ...
Al Teimi Ibrahim
Human fascioliasis is well documented throughout the world, both the acute and chronic phases of the disease have been well described. Cholelithiasis with obstructive jaundice and discovery of fasciola hepatica worms during surgical exploration is a frequent mode of first diagnosis of chronic fascioliasis. Here the presentation of six proven ...
Al Teimi I N - - 1995
Human fascioliasis is well documented throughout the world, both the acute and chronic phases of the disease have been well described. Cholelithiasis with obstructive jaundice and discovery of fasciola hepatica worms during surgical exploration is a frequent mode of first diagnosis of chronic fascioliasis. Here the presentation of six proven ...
Shojaku H - - 1995
In order to clarify the characteristics of severe cases of Meniére's disease (MD), we analyzed various epidemiological factors such as sex ratio, past history, complication, cause of onset of vertiginous attacks, etc., in a series of 958 patients with definite MD. Data were obtained from the three Japan-wide surveys of ...
Goldfarb D - - 1994
Lyme disease is an important consideration in the differential diagnosis of patients seen by the otolaryngologist. Facial paralysis is the most common sign. The otolaryngologist may also see patients with temporal mandibular joint pain, cervical lymphadenopathy, facial pain, headache, tinnitis, vertigo, decreased hearing, otalgia and sore throat. The incidence is ...
Nyrop M - - 1994
Kimura's disease is a chronic inflammatory disease which often presents as a tumour-like swelling in the head and neck region with or without lymphadenopathy. Most cases have been described predominantly in Chinese and Japanese people. The lesion is benign, but it may easily be mistaken for a malignant tumour. Kimura's ...
Williams D J - - 1994
This case report describes the unusual complications of a simple fall in a person with a profound neurological disorder, Hallervorden-Spatz disease. The fall produced a laceration of the forehead, skull fractures and severe occipital contrecoup contusions. Such contrecoup contusions are rare and may be a feature of this case because ...
Saunders C J - - 1994
When a single case of legionnaires' disease is reported, it should be investigated to check whether or not it is linked to other cases or part of an outbreak. The investigation includes confirmation of the diagnosis, tracing the patient's movements during the incubation period, and reporting the case to the ...
Healy C M - - 1994
In this article two case reports of pyostomatitis vegetans are presented. Both cases were associated with inflammatory bowel disease and one case was also associated with liver dysfunction. It has recently been reported that there may be a link between liver dysfunction and pyostomatitis vegetans. The management of the condition ...
Ehrenpreis S J - - 1994
Intraventricular hemangioblastomas are exceptionally rare. Of the cases described in the literature, very few were associated with von Hippel-Lindau disease. We present a highly unusual case of a fourth ventricular hemangioblastoma associated with a pheochromocytoma and a renal medullary fibroma. This may represent a forme fruste of the von Hippel-Lindau ...
Mackey S L - - 1994
Knuckle pads are well circumscribed thickenings of the skin over the metacarpophalangeal and, more commonly, the proximal interphalangeal joints. Although the association with several other clinical syndromes including Dupuytren's disease is well documented, most cases are idiopathic. We present a case of knuckle pads and briefly review the history and ...
Jackson J L - - 1994
There are 36 reports in the English-language literature of Kawasaki disease in adults. We present two additional cases, in one of which retinal vasculitis developed, a previously unreported complication antemortem. We report the first use of intravenous gamma globulin in the United States for treatment of adult-onset Kawasaki disease and ...
Thornbury W C WC - - 1994
Fabry disease is a rare lipid storage disorder, often silent until adulthood. We report the case of a rural, primary care patient whose initial presentation was that of progressive weakness from anemia. The anemia was determined to be of renal origin, and led to a diagnosis of Fabry disease. Although ...
Salcman M - - 1994
Calcium pyrophosphate deposition disease is a relatively uncommon arthropathy characterized by the clinical features of pseudogout, the radiographic manifestations of chondrocalcinosis, and the pathological deposition of calcium pyrophosphate crystals in both hyaline and fibrocartilage. Symptomatic involvement of the spine by calcium pyrophosphate deposition disease is rare except by nodular deposition ...
Schubert F - - 1994
A case is presented of echogenic tumours in the spleen of a patient with Niemann-Pick disease of the type B (or adult) type. A search of the literature revealed that a similar appearance has previously been reported in only one other case of Niemann-Pick disease, which was a type C.
Abbott S L - - 1994
Vibrio hollisae, one of the more recently described halophilic Vibrio species, is infrequently associated with gastrointestinal disease and only rarely recovered from individuals presenting with gram-negative sepsis. In this report we describe two cases of severe gastrointestinal disease associated with V. hollisae in otherwise healthy individuals. In one of these ...
Tanabe M - - 1994
The case of a 39-year-old man with von Recklinghausen's disease, presenting with emaciation and a marked increase in serum growth hormone concentration, is presented. Neuroradiological and histological examination confirmed anaplastic astrocytoma in the optic chiasm-hypothalamic region. This is a rare case of diencephalic syndrome and von Recklinghausen's occurring together in ...
Harada K - - 1994
Meningioangiomatosis is rare disease and is classified as hamartoma in central neurofibromatosis. Unlike most cases of meningioangiomatosis, the very rare case reported here was not associated with von Recklinghausen's disease. We could find only 12 previous cases reported in the literature. A review was carried out of the clinical features, ...
Horowitz H W - - 1994
Myositis due to the etiologic agent of Lyme disease, Borrelia burgdorferi, has been reported nine times in the English-language literature; there has been but a single report of exacerbation of dermatomyositis due to B. burgdorferi in a patient with known dermatomyositis. Multiple infectious agents, but not B. burgdorferi, have been ...
Tavin M E - - 1993
Presented herein is a case report of sudden sensorineural hearing loss in the setting of haemoglobin SC disease. The relationship of the two is rare; the authors have found that this is only the second report in the literature. In this instance, partial exchange transfusions were performed in an attempt ...
Lyu R K - - 1993
We report on a 12-year-old Chinese child with type C Niemann-Pick disease, who presented primarily with neurologic symptoms. He started to develop ataxia and dysarthria at the age of six years. Dementia, dysphagia, dystonia and seizures, in that sequence, followed within a couple of years. He was anarthric and bedridden ...
Al-Bunyan M - - 1993
Two hundred and twenty-one Saudi patients admitted for stroke in King Khalid University Hospital between 1982 and 1987 were evaluated clinically and by laboratory and radiological investigations. Twelve patients were found to have leukoraiosis on brain CT and a clinical picture compatible with Binswanger disease (subcortical arteriosclerotic encephalopathy). Arterial hypertension ...
Yörüko─člu Y - - 1993
Thromboangiitis obliterans (TAO) is an occlusive vascular disease traditionally known to be almost exclusive to young male smokers. The disease was considered to be extremely rare in women, seen only as isolated, novel case reports in the literature. In the past decade, however, a dramatic increase in the incidence of ...
Kaur M - - 1993
Niemann-Pick group of diseases are rare autosomal recessive disorders of lysosomal enzymes. These are divisible into six types depending on clinical and biochemical features. On the basis of sphingomyelinase assay in five cases of Niemann-Pick disease, three cases were classified as type IA, one as type IS and one as ...
Mangili G - - 1993
We report the case of a woman with a familial history of gestational trophoblastic disease who developed repeated partial and complete moles after fertilization by her husband and heterologous assisted conception. This case has interesting etiologic implications, but it is difficult to make any extrapolation from this very peculiar case ...
Williams M D - - 1993
An infant with the rare association of colon atresia, total colonic Hirschsprung's disease, and tetralogy of Fallot is presented. While Hirschsprung's disease associated with atresia of the colon has been reported five times previously, this is the first case with associated congenital cardiac disease. As in previous reports, initial operations ...
Wabinga H R - - 1993
Biopsy and autopsy protocols revealed that between 1972 and 1981, 85 cases of scleroma were diagnosed in Uganda. The disease was found to affect females more than males, and was found to be more common in the middle aged. Scleroma occurred in the nose in 96% of cases and presented ...
Matsumura Y - - 1993
The skin lesions in epidermolysis bullosa acquisita (EBA), a mechanobullous disease, often show acral distribution. Recently, we experienced a case of EBA in which most of the skin lesions were located on the trunk. We reviewed the distribution of the skin eruptions in 58 reported cases of EBA. Although the ...
Danielsson L G - - 1993
To define radiographic criteria, the radiographs of all patients diagnosed with coxarthrosis during the year 1951 were reviewed. Structural or joint space changes, evident radiographically in one of every seven cases in 1951, persisted at the time of the review in 1962. In the remaining cases, the diagnosis had been ...
Cohen M C - - 1993
Acquired Hirschsprung's disease is a rare and controversial form of colonic aganglionosis. Little is known about its aetiology and pathogenesis. We report five cases encountered amongst 173 long-term follow-up patients treated for classical Hirschsprung's disease between 1957 and 1990 at the Red Cross Children's Hospital, Cape Town, and review the ...
Miyata T - - 1993
Angiosarcoma of the spleen is a rare disease, and the prognosis of this disease is extremely unfavorable. We herein review the case of a 45-year-old Japanese woman, who received a combined chemotherapy with cyclophosphamide, Adriamycin, vincristine, and prednisone after splenectomy and experienced a good response. The various types of chemotherapy ...
Zaloznik A J - - 1992
Gastric involvement in Hodgkin's disease is rare. A case of gastric Hodgkin's disease occurring after autologous bone marrow transplantation is presented. A retrospective review of 339 cases of Hodgkin's disease in the Tumor Registry at Brooke Army Medical Center revealed six additional cases of documented gastric involvement. These six cases ...
Matteson E L - - 1992
Lyme disease has been reported in Minnesota since 1980. Until now, it has not been regarded as endemic in Olmsted County. We reviewed the medical records of all 68 cases of Lyme disease diagnosed in residents of Olmsted County for 1980-1990. Only 17 of the 68 cases met Centers for ...
Ciofu C - - 1992
The authors report a case of a 3-month-old infant with a very rare association: cystic fibrosis and Kawasaki disease. The clinical picture is atypical but cardiovascular signs consist of cardiomegaly, sick sinus syndrome and Q waves in D II, D III and AVF. The diagnosis is confirmed by the pathological ...
Weinstein S M - - 1992
No one discounts the cruel nature of the Acquired Immunodeficiency Syndrome epidemic or the pain and devastation left by the virus that brings a lingering death to people in the prime of life. And no one dismisses the horrifying surge in the number of cases over the past decade. In ...
Smoller B R - - 1992
BACKGROUND: Woringer-Kolopp (W-K) disease is a rare, localized, histologically malignant, but clinically indolent lymphoproliferative disorder. Most authors have regarded W-K disease as a variant of mycosis fungoides. However, a recent case suggests that W-K disease may represent a spectrum of lymphoproliferative disorders that may not be related to mycosis fungoides. ...
Meneghelli U G - - 1992
Polycystic hydatid disease occurs in neotropical zones and is caused by Echinococcus vogeli. The paca, a wild rodent, is the intermediate host and the final host is the dog. Seven cases of polycystic hydatid disease autochthonous to the Brazilian Amazon region are described. The disease was polycystic in all cases ...
Motomura N - - 1992
Lateral hemispheric asymmetries (LHA) of I-123 IMP single photon emission tomography (SPECT) in senile dementia of Alzheimer's type (SDAT) were investigated. Significant left-right asymmetries were found by SPECT imaging in 13/17 SDAT patients. LHA were found in mild as well as in moderate or severe cases of SDAT. No relationships ...
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