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Results 451 - 500 of 575
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Edwards O P - - 1989
Autosomal dominant polycystic kidney disease presenting in the fetus or newborn is rare, only 22 cases having been reported in the literature. A case is reported of a premature newborn infant with severe renal involvement and extrarenal associated abnormalities. The literature is reviewed, and the importance of considering this entity ...
Joyce A P - - 1989
Prurigo pigmentosa is an uncommon skin disease first reported from Japan where it has gained recognition as distinct cutaneous disease characterized by rapid response to dapsone therapy. Recently, a few reports of prurigo pigmentosa have appeared in the western literature. American-born white man and review the literature pertaining to this ...
Engelkens H J - - 1989
Early yaws in a 9 year old girl from Ghana, diagnosed as imported disease in The Netherlands is reported. She had lived in The Netherlands for six months. Tropical non-venereal treponematoses are rarely seen in Europe, and only a few case reports have been published. Migration and travelling may confront ...
Franzblau A - - 1989
Asbestos-associated rounded atelectasis is a nonmalignant radiographic consequence of asbestos exposure that can mimic neoplasia. It is infrequently mentioned in reviews of the radiographic features of nonmalignant asbestos-associated disease. Distinguishing it from malignant disease without resorting to chest surgery is important. This report presents a case of such atelectasis, and ...
Berth-Jones J - - 1989
Cholinergic pruritus and cholinergic erythema are relatively rare conditions believed to represent variants of cholinergic urticaria. We report an extremely severe and unusual case demonstrating features of both these variants before evolving into more classical cholinergic urticaria. This strongly supports the view that all three syndromes are variations of the ...
Byrne E J - - 1989
Fifteen cases of diffuse Lewy body disease were diagnosed on pathological grounds during a single year in one health district. The range and frequency of clinical features contrast strikingly with previous reports. The majority of cases presented with classical levodopa-responsive Parkinson's disease either alone (6 cases) or with mild cognitive ...
Markowitz R L - - 1989
Cerebral and retinal vascular disease are rare complications of inflammatory bowel disease. Most reports are of adult patients, with only seven instances described in children. The eighth case, a 14-year-old boy with ulcerative colitis and cerebral venous thrombosis is reported in whom the diagnosis was confirmed by magnetic resonance imaging. ...
Leggiadro R J - - 1989
We have reported the epidemiologic investigation and subsequent control measures precipitated by the occurrence of two temporally related cases of invasive meningococcal disease in a single day-care center classroom. A review of the literature indicates that day-care center contacts of patients with invasive meningococcal disease are at increased risk for ...
Deasy J - - 1989
This is a case report of the simple form of Caroli's disease in a 36 year old Irish woman who has extensive bilobar involvement without congenital hepatic fibrosis or portal hypertension. The difficulty of diagnosis and the intractable nature of the disease are emphasised and recent improvements in diagnosis and ...
Griffiths A M - - 1989
Ten cases of gastroduodenal inflammation were diagnosed by endoscopy among a series of 196 children with evidence of Crohn's disease involving other regions of the intestinal tract. Endoscopic and histologic confirmation of upper gastrointestinal tract involvement was performed only in those cases with suggestive symptoms. The mean age at presentation ...
Sampaio J S - - 1989
We report 5 cases of severe Peyronie's disease treated by a new procedure. It consists of making parallel I-shaped incisions on the dorsal face of the penis so that the shortened part of the albuginea can increase. The 2 defects are covered with 2 patches of dura mater. All the ...
Stahle J - - 1989
The histopathological picture in Meniere's disease was described for the first time in 1938, in two independent reports. One was by Hallpike & Cairns in Great Britain, and the other by Yamakawa in Japan. Selections of illustrations from these two reports have been compiled and compared.(ABSTRACT TRUNCATED AT 250 WORDS)
Wong H C - - 1989
This case report presents both the clinical and the histopathological features of the oldest patient on record with ophthalmic manifestations of Rosai-Dorfman Disease. An unusual feature, which has not been previously reported, is involvement of the cornea with subsequent perforation of the globe. The absence of lymphadenopathy is discussed.
Benisovich V - - 1988
The case of a patient with an unusual skin disorder--progressive, atrophying, chronic, granulomatous dermohypodermitis (PACGD)--who developed Hodgkin's disease is reported. A review of the literature revealed only two other cases of PACGD, one of which affected a patient who also was found to have Hodgkin's disease. In an additional report, ...
Marano S R - - 1988
A case of recurrent Lhermitte-Duclos disease (dysplastic gangliocytoma of the cerebellum) in a child is described with a summary of the clinical presentation and associated malformations, and a review of other cases reported in the literature. The histological examination and electron microscopic findings, with special reference to the cytological changes ...
Hicks G W - - 1988
Delayed endolymphatic hydrops is a disease entity that can be differentiated from Meniere's disease. This condition was first reported simultaneously by Nadol, et al. and Wolfson and Leiberman, with further clarification by Schuknecht. The disease is characterized by a profound sensorineural hearing loss in one ear, with the onset of ...
Plotnicov N A - - 1988
Madelung's disease, benign symmetric lipomatosis, is a rare disease of undetermined cause characterized by symmetric deposits of diffuse adipose tissue on the cheeks, the neck, and the upper trunk. This article outlines our experience with four patients and presents a case report of a specifically remarkable affectation that agrees with ...
Adams P C - - 1988
Hemochromatosis is a disease in which the inappropriate absorption of iron over 30-40 yr results in tissue iron overload and the development of cirrhosis of the liver, diabetes, hypogonadism, arthropathy, and skin pigmentation. We present an infant who died at 2 days of age, and who was found to have ...
Ashby M A - - 1988
We report here a case in which a frontotemporal meningeal tumor was found to be an isolated, apparently primary, deposit of nodular sclerosing Hodgkin's disease in an otherwise well man. The presentation of Hodgkin's disease as a primary, solitary intracranial lesion is rare; only 13 cases have been found in ...
Jung E G - - 1988
Patients who appear to warrant the diagnosis of neurofibromatosis in some sense, but who do not meet the current inclusive criteria for von Recklinghausen disease (NF-1) are uncommon, but not rare. This report describes the clinical findings of 7 such cases and compares them to 32 other cases from the ...
Berman S M - - 1988
Urachal disorders are uncommon and present with varied appearances. Three cases of urachal disease, one congenital and two acquired, are reported. Each case is representative of the symptoms and findings of its respective category. A review of the literature is presented. A basic understanding of urachal development is necessary to ...
Holmes P F - - 1988
Aspergillus discitis is a rare disease that usually occurs in immunocompromised hosts. In the one case reported in the orthopedic literature surgical debridement was required. Two additional cases, which occurred in intravenous drug abusers, are reported here. One case is unique in the orthopedic literature in that eradication of the ...
Frija J - - 1987
Twelve cases of recurrences of Hodgkin's disease on the chest wall, associated with three breast lesions and three diaphragmatic lesions, were studied by computed tomography (CT). Although the chest radiographs of all the patients were abnormal, CT was more accurate than clinical and other radiological examinations in delineating the lesions ...
Pomeroy C - - 1987
Selenomonas species are crescent shaped Gram-negative bacilli with a characteristic tuft of flagella located on the concave surface. They are normally found in human gingiva or the rumen of herbivores. The first case of Selenomonas bacteraemia to be reported in a patient immunocompromised by malignant disease is described and the ...
Hattori T - - 1987
A case of facial palsy was reported initially in 1974 by Murayama as one of the neurological manifestations in Kawasaki disease. Thereafter, an additional nine case have been documented in Japan. This facial palsy, in the revised "Diagnostic Guideline of Kawasaki Disease" released in 1984, has been added recently as ...
Ruzicka T - - 1987
Benign symmetric lipomatosis Launois-Bensaude is a disease rarely reported in the American literature and not mentioned in the standard English textbooks of dermatology. It seems, however, to be relatively common in Europe. Between 1981 and 1985 we examined twelve patients, and a number of case reports have been published in ...
McCabe R E - - 1987
Lymphadenopathy is the most frequent clinical manifestation of acute acquired infection with Toxoplasma in the immunocompetent individual. One hundred seven cases of histologically verified toxoplasmic lymphadenitis were reviewed in an effort to determine the usual modes of clinical presentation and the incidence of extranodal disease. Toxoplasmic lymphadenitis most frequently involved ...
Conti Nibali S - - 1987
This is the first report of obesity in an untreated coeliac patient diagnosed at the age of 5.1 years according to the criteria of the European Society for Paediatric Gastroenterology. Diagnosis of coeliac disease was suspected on the basis of recurrent episodes of abdominal pain and of family history. Gluten-free ...
Thie A - - 1987
The case of a German patient who was treated with two courses of praziquantel for parenchymal cerebral cysticerosis (CC) is reported. Efficacy of the treatment could not reliably be distinguished from the natural course of the disease. After a brief review of the literature concerning problems with assessment of the ...
Pretorius D H - - 1987
Autosomal dominant polycystic kidney disease (ADPKD), once thought to be a disease of the adult, is now being reported with increasing frequency in childhood. We report five cases and review eight cases from the literature of ADPKD diagnosed in the fetus or the young infant by sonographic evaluation and a ...
Lifshitz T - - 1987
A case of early childhood Coats's disease in a ten-month-old boy is presented. The lactic dehydrogenase aqueous:serum ratio was very high (6:1). A ratio higher than 3:1 in Coats's disease or in any other eye infection has never been reported except in cases of retinoblastoma. Since retinoblastoma does not always ...
Spanjaard L - - 1987
Case histories of 692 patients with meningococcal disease due to serogroup B, C, or W (W-135) were reviewed to study the association of the serotypes 2a and 2b with the course of disease. The case-fatality rate in group B disease was significantly associated with serotype 2b (B:2b) strains (P = ...
Kristoferitsch W - - 1987
A case of slowly progressing cerebellar syndrome and pathologically confirmed adult coeliac disease is presented. Neurological symptoms progressed although the patient had no enteric complaints. This case seems to be identical with 18 previously reported cases of encephalopathy and adult coeliac disease. However, the aetiology and pathogenesis of the encephalopathy ...
Chen Y M - - 1987
Cowden's disease, or multiple hamartoma syndrome, is an uncommon condition with characteristic mucocutaneous lesions associated with abnormalities of the breast, thyroid, and gastrointestinal tract. We describe a 51-year-old man with hyperplastic polyposis of the entire alimentary tract as the most prominent feature of this disease. We also present a review ...
Müller W - - 1987
During a one-year period we could observe 3 children with the rare disease of plastic bronchitis. Two of them showed a symptomatic form, one with constrictive pericarditis, the other with bronchial asthma as primary diseases. No underlying disease could be found in the third case. Bronchial casts had to be ...
Rinaldi M G - - 1987
Curvularia lunata is a saprobic dematiaceous mould that resides primarily in soil (Ellis, 1966). Reports of human disease caused by this organism are rare but include: endocarditis, brain abscess, skin infections, onychomycosis, keratitis, pneumonia, disseminated disease, mycetoma, allergic bronchopulmonary disease, and one case of sinusitis. Since 1983, we have encountered ...
Zahra M - - 1986
We are presenting a case history of a patient with advanced Hodgkin's disease, who had secondary involvement of his middle ear. To our knowledge this is the first case report of such clinical presentation where radiation therapy was of good help for bringing about symptomatic relief. Possible routes of spread ...
Schairer C - - 1986
The relation between methylxanthine consumption and biopsied benign breast disease was investigated by using data from a case-control study which included 1,569 cases and 1,846 controls identified between 1973 and 1980 through a nationwide screening program. There was no evidence of an association between methylxanthine consumption and benign breast disease ...
Gal R - - 1986
A case of lymphoid hypophysitis in a woman who died during labor is presented. From a review of the 14 previously reported cases it is apparent that this is a specific disease entity, that it involves only woman, especially in association with pregnancy, and that it may have a fatal ...
Emtage J B - - 1986
Malignant seeding on the needle tract of a perineal prostatic biopsy is a rare complication. A review of the literature revealed only 7 cases. Herein another case is reported. Our patient, like all other cases reported, suffered from high-grade, high-stage disease and the perineal extension did not upstage his disease. ...
Clark A W - - 1986
We report two cases of dementia in which cortical degeneration with widespread swollen chromatolytic neurons (SCN) was the dominant pathologic feature. Each patient had received the diagnosis of Alzheimer's disease on the basis of clinical findings. There was no deficit of cortical choline acetyltransferase activity, assayed in one case, or ...
Viegas S F - - 1986
Triggering of the thumb due to de Quervain's Disease has not been reported in an adult, and only one case in a child has been documented in the literature. Two cases of trigger thumb that were due to stenosing tenosynovitis in which the extensor pollicis brevis tendon triggered in a ...
Iguchi Y - - 1986
Kimura's disease, eosinophilic granuloma of soft tissues, is a chronic inflammatory condition and appears as subcutaneous tumor-like nodules in the head and neck regions. Histopathologically, it is characterized by the presence of lymphoid follicles, marked infiltration of eosinophils, fibrosis and vascular proliferation. This disease occurring in the orofacial region is ...
Ylitalo V - - 1986
The case reports of two Swedish girls with initially pseudostationary clinical pictures, one simulating ataxic and the other dyskinetic cerebral palsy, are presented. It was eventually revealed that they had a slowly progressive encephalopathy with pronounced gross motor disability and signs of severe dyskinesia, but only mild intellectual delay. Electron ...
Nilssen D E - - 1986
Four cases of antiglomerular basement membrane (antiGBM) antibody mediated disease with unusual features are presented. Lung involvement was absent in one patient whereas the other 3 had Goodpasture's syndrome. Recognition of the nature of the disease was delayed in all cases, due to occurrence during pregnancy in one case and ...
Tamburrini O - - 1986
Intestinal malrotation and Hirschsprung's disease may be associated with other congenital anomalies. However, the association of Hirschsprung's disease with intestinal malrotation has been recently pointed out and sporadic cases are reported in the literature. We describe a case of such an association in a baby with asymptomatic malrotation and emphasize ...
Nishigori C - - 1986
Two cases of penis tuberculides are described. Although this disease once used to be comparatively common in Japan, the number of people affected by the disease has recently decreased as the prevalence of tuberculosis has fallen. However, we can still find a few cases in the Japanese literature every year. ...
Belfiglio E J - - 1986
Myospherulosis is a recently discovered disease apparently caused by the placement of mineral oil- or petrolatum-based products into various tissues. Terra-Cortril (a tetracycline/steroid ointment in a petrolatum base) on Gelfoam has been placed in the sockets of surgically removed third molars in an attempt to eliminate the occurrence of dry ...
Dicken C H - - 1985
Malignant pyoderma is a destructive, ulcerating skin disease that occurs chiefly in young adults. Only eight cases of this rare disease have been reported. The head and neck have been involved in all cases, and a predilection for the periauricular region has been noted in several of the cases. Although ...
Ueda N - - 1985
This is a case report of a purported panencephalopathic type of Creutzfeldt-Jakob (C-J) disease in a 61-year-old Japanese farmer. He died nine months after the onset of clinical symptoms. This variety of C-J disease was named and reported in 1981 by Mizutani. The characteristic feature is extensive degeneration of cerebral ...
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